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Superficial Siderosis with Peripheral Dizziness: Report of 2 Cases
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Tae-Hoon Kim, Jin-Hyuk Huh, Moon-Suh Park, Jae-Yong Byun
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Res Vestib Sci. 2018;17(2):60-66. Published online June 15, 2018
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DOI: https://doi.org/10.21790/rvs.2018.17.2.60
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Abstract
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- Superficial siderosis (SS) of the central nervous system is a rare disease, which is caused by the accumulation of iron from the hemoglobin in the superficial layer of the brain, spinal cord, and central parts of cranial nerves. The etiology of SS is the accumulation of hemosiderin in the subarachnoid space due to chronic or repeated hemorrhage resulting in progressive and irreversible neurological dysfunction. The cause of the disease is aneurysm, trauma, tumor, and vascular malformation. In most cases, the cause of bleeding is unknown. Clinical features include sensorineural hearing loss, cerebellar ataxia, and myelopathy. Until now, magnetic resonance imaging (MRI) has only been diagnosed and there is no standardized treatment. We will investigate clinical features and MRI findings of SS disease in the central nervous system using 2 patient cases.
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- A Case of Patient with Bilateral Cochleovestibular Function Loss due to Infratentorial Superficial Siderosis
Gyuman Lee, Youngmin Mun, Dae Bo Shim Research in Vestibular Science.2023; 22(3): 83. CrossRef
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말초성 어지럼증으로 표현된 Superficial siderosis 환자 2례
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Tae-hoon Kim, Jin-Hyuk Huh, Moon-suh Park, Jae Yong Byun
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Received May 31, 2018 Accepted June 1, 2018 Published online June 1, 2018
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[Accepted]
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Abstract
- Superficial siderosis(SS) of the central nervous system is a rare disease, which is caused by the accumulation of iron from the hemoglobin in the superficial layer of the brain, spinal cord, and central parts of cranial nerves. The etiology of SS is the accumulation of hemosiderin in the subarachnoid space due to chronic or repeated hemorrhage resulting in progressive and irreversible neurological dysfunction. The cause of the disease is aneurysm, trauma, tumor, and vascular malformation. In most cases, the cause of bleeding is unknown. Clinical features include sensorineural hearing loss, cerebellar ataxia, and myelopathy. Until now, MRI has only been diagnosed and there is no standardized treatment.
We will investigate clinical features and MRI findings of superficial siderosis disease in the central nervous system using 2 patient cases.
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