Osteomas arising from the internal auditory canal (IAC) and locating in the cerebellopontine angle (CPA) are rare. These tumors may cause compression of the IAC with varying degree of hearing loss, vertigo, and tinnitus but sometimes asymptomatic. Here we present a 60-year-old female patient presented with a hearing loss of sudden onset in her right ear and recurrent dizziness of whirling type. Magnetic resonance imaging and computed tomography revealed CPA osteoma arising from the porus of the IAC. Osteomas should be considered as differential diagnosis in patients with sudden hearing loss and vertigo. Key Words: Osteoma; Cerebellopontine angle; Hearing Loss, Sudden