Meniere disease (MD) is an inner ear disorder characterized by episodic vertigo, fluctuating hearing loss, tinnitus and aural-fullness. Even though the pathologic process is not clearly understood, it well correlated with distortion of the membranous labyrinth by endolymphatic hydrops. The clinical presentation is the most important for diagnosing MD and its treatment option range from lifestyle modification or from medical therapy to ablation surgery according to the characteristics of patients with MD. This review describes the pathophyology of MD, and its evaluation and treatment.