Abstract

Autoimmune inner ear disease(AIED) is a rare disease, accounting for <1% of all case of hearing impairment or dizziness. It is characterized by sensorineural hearing loss(SNHL) or vestibular dysfunction that result from an immune-mediated process. Clinical feature of AIED is SNHL that progresses over weeks to months and fluctuating hearing symptoms. Because there’s no diagnostic laboratory test, clinical features and re-sponse to immunosuppressive therapy were important for diagnosis of AIED. Many disease such as sudden sensorineural hearing loss and Meniere's disease may also mimic AIED, a broad differential must be maintained in patients suspected of having AIED. We report a case of a 46-year-old female who presented with sudden hearing loss and vertigo. We could diagnose her as AIED with systemic lupus erythematous(SLE). The symptoms were improved treated with steroids.

• Keywords: Autoimmune inner ear disease; ystemic lupus erythematous; Sensorineural hearing loss;